The "harlequin" sign and congenital Horner's syndrome.

The "harlequin" sign and congenital Horner's syndrome.

When trying to establish the likely anatomical site (preganglionic or postganglionic) of a lesion causing congenital Horner's syndrome, the distribution of facial flushing (the "harlequin" sign), may be seen. In babies and young children, facial flushing is a relatively simple clinical sign to demonstrate, compared with facial sweating. In unilateral facial flushing the areas that do not flush ...

Harlequin Syndrome

Harlequin Syndrome in Cluster Headache.

A 63-year-old male experienced 3 years of excruciating, right retro-orbital, 15–90 minute headaches occurring 1 to 3 times daily associated with ipsilateral lacrimation, ptosis, and facial congestion. The episodes began after a complicated right root canal procedure. He also reported separate episodes of distinct left sided facial flushing triggered by exertion as evidenced by a photo that he p...

Adams Oliver Syndrome and Congenital Deafness

Admas-Oliver syndrome is a rare autosomal dominant disease of congenital development defects association with aplasia cutis. All of 81 reported cases were of 32 group families. These two cases had congenital scalp cutis aplasia with developmental defect and hypoplasia of left foot digits in case 1.Congenital deaf-mute in both can added to the past known findings in this syndrome. Thoracic defor...

Harlequin syndrome: the sudden onset of unilateral flushing and sweating.

Facial flushing and sweating were investigated in five patients who complained of the sudden onset of unilateral facial flushing in hot weather or when exercising vigorously. One patient probably suffered a brainstem infarct at the time that the unilateral flush was first noticed, and was left with a subtle Horner's syndrome on the side opposite to the flush. The other four had no other neurolo...